A Case of Von Recklinghausen's Disease (Multiple Neurofibromata) with Spontaneous Fractures *This Essay was awarded a Martyn Memorial Pathological Scholarship.
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چکیده
Although von Recklinghausen, in 1882, was the first to describe the pathology of the disease, it is interesting to note that one of our own countrymen, Robert W. Smith, after research in two cases, published an account of the condition in 1849. Von Recklinghausen, however, was the first to offer the now accepted theory of neuro-fibromatosis. The disease is characterized by multiple painless nodules in the skin, irregularly distributed over the
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The Histology of the Aortic Wall in Acute Rheumatism *This Essay was awarded the Martyn Memorial Pathological Scholarship for 1929.From the University Centre of Cardiac Research, General Hospital, Bristol.
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The case history is presented of a 61 year old man with von Recklinghausen's disease who developed a spontaneous haemothorax. In spite of being asymptomatic for five days after drainage, he died as a result of fatal sudden re-bleeding. The post mortem examination showed dissection and rupture of the left subclavian artery. Microscopically, disarrangement of smooth muscle and decrease of elastic...
متن کاملSpontaneous hemothorax caused by a ruptured intercostal artery aneurysm in von Recklinghausen's neurofibromatosis.
Aneurysms arising from an intercostal artery are very rare vascular malformations in von Recklinghausen's neurofibromatosis, which often have a silent clinical presentation and are difficult to diagnose before rupture. We report a case of von Recklinghausen's neurofibromatosis with massive hemothroax caused by spontaneous rupture of an intercostal artery aneurysm in a 29-year-old man. The diagn...
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